Predominantly Antibody Deficiency

Gene: WAS

Green List (high evidence)

WAS (Wiskott-Aldrich syndrome)
EnsemblGeneIds (GRCh38): ENSG00000015285
EnsemblGeneIds (GRCh37): ENSG00000015285
OMIM: 300392, Gene2Phenotype
WAS is in 16 panels

2 reviews

Zornitza Stark (Victorian Clinical Genetics Services; Australian Genomics)

Green List (high evidence)

Mode of inheritance
X-LINKED: hemizygous mutation in males, biallelic mutations in females

Phenotypes
Wiskott-Aldrich syndrome, MIM# 301000; Thrombocytopaenia, X-linked, MIM# 313900; Neutropenia, severe congenital, X-linked , MIM#300299

Abhijit Kulkarni (Monash Genetics)

Green List (high evidence)

Mutations in the WAS gene have been found in patients with Wiskott-Aldrich syndrome (#301000), X-linked thrombocytopenia (#313900), and X-linked severe congenital neutropenia (SCNX; #300299).

Missense mutations that cause WAS map primarily to the enabled (609061)/VASP (601703) homology-1 (EVH1) domain of WASP.

PMID: 34307257: Reported Wiskott-Aldrich Syndrome caused by extremely skewed X-Chromosome inactivation in a Chinese Girl.
Created: 21 Mar 2022, 9:45 p.m. | Last Modified: 21 Mar 2022, 9:45 p.m.
Panel Version: 0.11705

Mode of inheritance
X-LINKED: hemizygous mutation in males, biallelic mutations in females

Phenotypes
Congenital Neutropenia; Throbocytopenia; Immunodefeciency; Eczema

Publications

History Filter Activity

17 Nov 2019, Gel status: 3

Created, Added New Source, Set mode of inheritance

Zornitza Stark (Victorian Clinical Genetics Services; Australian Genomics)

gene: WAS was added gene: WAS was added to Predominantly antibody deficiency_MelbourneGenomics_AustralianGenomics_VCGS. Sources: Expert Review Green,Victorian Clinical Genetics Services,Melbourne Genomics Health Alliance Immunology Flagship Mode of inheritance for gene: WAS was set to Unknown